A collection of disease information resources and questions answered by our genetic and rare diseases information specialists for henochschonlein purpura. It affects children, mainly males, in 90% of cases the four main clinical features include purpura rash, abdominal pain, arthralgia and renal involvement. Its incidence is low in childhood with the exception of henoch schonlein purpura hsp and. In the skin, the disease causes palpable purpura small, raised areas of bleeding.
A case of hsp is reported in a 36yearold female with. Supportive care until recovery when there is little or no kidney involvement may include adequate hydration, rest, and overthecounter pain medication as needed for joint and abdominal pain due to inflammation. Hsp is usually selflimiting in 94% of children and 89% of adults. Schonleinhenoch purpura, anaphylactoid purpura rhumatoid purpura diagnosis diagnosis of hsp is established when at least 2 of the following 4 criteria are present. Protocolos diagnosticos y terapeuticos en pediatria. Henochschonlein purpura genetic and rare diseases information. Henoch schonlein purpura hsp is an immune mechanism leukocytoclastic vasculitis with small vessel involvement. Purpura schonlein henoch, nefropatia iga, vasculitis iga. Authors work related studies book searches payperview relevant portals online forums teaching files government policy.
Purpura, arthritis, and abdominal pain are known as the classic triad of henochschonlein purpura. Renal manifestations of henoch schonlein purpura in a 6 month prospective study. Precedidas por una infecciondel tracto respiratorio superiorpatologia mediada por elsistema inmuneinducida por factoresambientales. Some include gastrointestinal hemorrhage as a fourth criterion. Purpura occur in all cases, joint pains and arthritis in 80%, and abdominal pain in 62%. The disease is characterized by abnormal deposits of immunoglobulin a an antibody in the blood vessels, leading to their inflammation vasculitis. Henochschonlein purpura hsp is vasculitis of the small vessels, the most common vasculitis of the childhood and is uncommon in adults. Please use one of the following formats to cite this article in your essay, paper or report. Henoch schonlein purpura presenting as hemorrhagic vesicles and bullae. The vast majority of people with henochschonlein purpura hsp recover on their own within several weeks. Henochschonlein purpura hsp, also called immunoglobulin a vasculitis igav, is a vascular disease that primarily affects small blood vessels. The small vessels of the skin, joints, kidneys, and digestive organs are particularly involved. Longterm outcome and treatment academic dissertation to be presented with the assent of the faculty of medicine, university of oulu, for public discussion in the auditorium 12 of the department of paediatrics, on november 25th, 2005, at 12 noon oulun yliopisto, oulu 2005. Schonlein henoch enfermedades raras y patologias poco comunes.
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